Crouzon Syndrome: a case report

Crouzon syndrome in association with acanthosis nigricans

Crouzon syndrome is a rare inherited autosomal dominant syndrome characterized by craniosynostosis, midface hypoplasia. Acanthosis nigricans may be associated with Crouzon syndrome, but it differs from the classic crouzon syndrome. This is a report of a 30-year-old-woman who presented acanthosis nigricans coexist with crouzon syndrome.

کرانیوفاسیال دیسوستوزیس و گزارش یک مورد جراحی سندرم کروزون

The most important craniofacial dysostosis & syndromes are Crouzon, Apret, Pfeiffer.Carpenter Saether- Chotzen. The common characteristic is premature closure of cranial sutures, which result in Maxillofacial deformities. Perfect recognition and carefully evaluation are the most important points in their reconstruction surgery.Because the prevalence & surgical treatment of Crouzon syndrome is l...

The dentist’s role in diagnosing craniofacial dysostosis

Introduction: The Crouzon syndrome is a rare clinical condition that affects the craniofacial skeleton development. It accounts for about 4.8% of all the cases of craniosynostosis, and it is the most common syndrome presenting with craniosynostoses. The Crouzon syndrome’s early diagnosis is critical to avoid cranial hypertension as well as visual disturbances and blindness. Children who have Cr...

The Crouzan Syndrome-A Case Report Key Words: Craniofacial syndromes, Crouzon syndrome, Premature synostosis

Growth Hormone Deficiency in a Case of Crouzon Syndrome with Hydrocephalus

Crouzon syndrome is one of the most common craniofacial syndromes and is inherited as autosomal dominant with variable expression. We report an 11 and a half-year-old boy with Crouzon syndrome with severe growth retardation. He had hydrocephalus since infancy and recently suffered from frequent dizziness. His bone age was only 5 years according to the Greulich and Pyle atlas. Magnetic resonance...

Crouzon syndrome - A rare case report

Crouzon syndrome is the most common syndrome among the craniosynostosis group. Crouzon syndrome accounts for about 4.8% of all of them. It commonly has autosomal dominant inheritance with complete penetrance and variable expressivity from subtle to severe forms and characterized by craniosynostosis, exophthalmos, and hypoplastic maxilla with relative mandibular prognathism. Mutation of the fibr...